Search bioRxiv⌕ Search

bioRxiv · 10.1101/513135

Phosphorylation of mitochondrial matrix proteins regulates their selective mitophagic degradation

Abstract

Mitophagy is an important quality control mechanism in eukaryotic cells, and defects in mitophagy correlate with aging phenomena and neurodegenerative disorders. It is known that different mitochondrial matrix proteins undergo mitophagy with very different rates, but to date the mechanism underlying this selectivity at the individual protein level has remained obscure. We now present evidence indicating that protein phosphorylation within the mitochondrial matrix plays a mechanistic role in regulating selective mitophagic degradation in yeast, via involvement of the Aup1 mitochondrial protein phosphatase, as well as two known matrix-localized protein kinases, Pkp1 and Pkp2. By focusing on a specific matrix phosphoprotein reporter, we also demonstrate that phospho-mimetic and non-phosphorylatable point mutations at known phosphosites in the reporter increased or decreased its tendency to undergo mitophagy. Finally, we show that phosphorylation of the reporter protein is dynamically regulated during mitophagy, in an Aup1-dependent manner. Our results indicate that structural determinants on a mitochondrial matrix protein can govern its mitophagic fate, and that protein phosphorylation regulates these determinants.\n\nSignificance statementMitochondrial dysfunction underlies many age-related human pathologies. In normal cells, defective mitochondria are often degraded by mitophagy, a process in which these mitochondria are engulfed in autophagosomes and sent for degradation in the lysosome/vacuole. Surprisingly, studies on mitophagy in diverse eukaryotic organisms reveal an unexpected dimension of protein-level selectivity, wherein individual protein species exhibit divergent rates of mitophagic degradation. In this manuscript, we show that this surprising intra-mitochondrial selectivity can be generated by differential phosphorylation of individual mitochondrial protein species, and we identify mitochondrial phosphatases and kinases which contribute to this regulation. By identifying a mechanism which regulates the intra-mitochondrial selectivity of mitophagic degradation, our findings open the door to potential manipulation of the quality control process in the future.

Source connections

Explore related subjects

Keep this discovery

Explore connections, maps & timelines

BibTeXRIS

Kolitsida, P., Zhou, J., Rackiewicz, M., Dengjel, J., Abeliovich, H.. 2019-01-09. Phosphorylation of mitochondrial matrix proteins regulates their selective mitophagic degradation. https://doi.org/10.1101/513135

Cite the original work for its findings. Save a collection to share your selection of sources.

KEEP EXPLORING

Related preprints

Platycodin D2 Targets Vimentin to Suppress Fibroblast-Myofibroblast Transition: A Novel Therapeutic Strategy Against Pulmonary Fibrosis

Background Pulmonary fibrosis is a progressive lung disease characterized by excessive extracellular matrix deposition and irreversible decline in lung function with limited effective therapeutic targets. Vimentin, a type III intermediate filament protein, plays a critical role in fibroblast activation and fibrogenesis, representing a promising drug target. Methods Novel vimentin ligands were screened via virtual screening. SPR assay verified compound-vimentin binding affinity. CETSA and CD spectroscopy analyzed protein structural changes after compound binding. In vitro FMT model and in vivo bleomycin-induced pulmonary fibrosis model were used to assess antifibrotic effects, and mutagenesis assays identified key binding amino acid residues. Results Platycodin D2 (PD2) from Platycodon grandiflorus was identified as a novel high-affinity vimentin ligand (Kd = 392.8 nM). PD2 binds vimentin directly, alters its secondary structure and induces insoluble aggregation. It effectively inhibits TGF-{beta}1-induced FMT in vitro and mitigates bleomycin-induced pulmonary fibrosis in vivo, reducing collagen deposition and improving animal survival. Critically, mutagenesis validation confirmed that key residues (Glu138 in chain A, Glu132 and Glu143 in chain B, as well as Glu50 and Arg54 in chain C) are essential for this interaction. Conclusions Our findings establish PD2 as a novel pharmacological inducer of aberrant vimentin aggregation, presenting a distinct target-driven strategy for antifibrotic drug development.

cell biology↗

Diversification of budding yeast polarization dynamics after compensatory experimental evolution

Essential cellular processes evolve under strong selection, yet protein networks underlying conserved functions can vary substantially. To what extent evolution constrains the intracellular dynamics of proteins performing essential functions is currently largely unknown. Here, we characterize budding yeast polarization phenotypes along a previously established evolutionary recovery trajectory, compensating for the loss of near-essential polarity gene BEM1. Through quantitative live cell imaging, we show that loss of BEM1 weakens and destabilizes polarization. Surprisingly, in recovered evolved lineages, protein dynamics change significantly compared to the ancestor: most notably, presence of main regulator Cdc42-GTP is strongly decreased, while polarisome member Spa2 localizes more slowly into mobile foci. Although separate phenotypic characteristics are only weakly constrained, we find evidence of effective protein-independent localization modes, revealing signs of convergence along the evolutionary trajectory. Together, our results show that evolution can restore global cellular function without conserving microscopic organization, instead giving rise to novel molecular phenotypes.

cell biology↗

Role of Very Long-Chain Fatty Acyl-Ceramides in Endocytic Uptake

Specialized endoplasmic reticulum (ER) subdomains termed ER sterol exit sites (ERSES), transiently contact endocytic sites to locally supply sterols, which in turn initiate actin polymerization and drive membrane invagination. Osh2, an oxysterol-binding protein (OSBP)-related protein (ORP), mediates the non-vesicular sterol transfer at ER-endocytic contact sites (ER-ECS). In search for additional ERSES components, we identified Fat1, a fatty acid (FA) transporter and acyl-CoA synthetase with specificity for very long-chain (VLC) FAs (C20-C26). Analysis of VLC-FA anabolic and catabolic pathways revealed a specific requirement for VLC fatty acyl-ceramides (VLCA-Cers) in the constriction of endocytic invaginations. Strikingly, the Cer synthase physically interacted with the endocytic machinery, pointing to a direct role of VLCFA-Cers in membrane remodelling. Consistent with this view, molecular dynamics and live-cell imaging of a Cer probe indicated that the ORPs Osh1 and Osh3 contribute to Cer export from at ER-ECS and and that their depletion recapitulates the endocytic defects observed in the absence of VLCFA-Cer. Our findings establish that local transport of VLCA-Cers is required for endocytic budding and reveal ERSES as hubs where Cer and sterol biosynthesis and transport converge

cell biology↗