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Zurawska-Plaksej, E.

Publications and source records attributed to Zurawska-Plaksej, E..

2 recordsLinked to original sources

A-beta-induced distress of astrocytes triggers Alzheimer disease pathology through non-canonical delta secretase activity

The importance of astrocytes for Alzheimer disease (AD) pathology is increasingly appreciated, yet the mechanisms whereby this cell type impacts neurodegenerative processes remain elusive. In a genetic mouse model with diminished astrocyte stress response, even low levels of amyloid-{beta} trigger astrocyte reactivity, resulting in brain inflammation and massive amyloid and tau pathologies. This dysfunctional response of astrocytes to amyloid-{beta} acts through activation of {delta} secretase, a stress-induced protease implicated in both amyloid and tau-related proteolytic processing. Our findings identify a failed astrocyte stress response to amyloid-{beta} as an early inducer of amyloid and tau co-morbidity, a noxious process in AD acting through a unique non-canonical secretase pathway.

neuroscience↗

Interaction of sortilin with apolipoprotein E3 enables neurons to use long-chain fatty acids as alternative metabolic fuel

Sortilin (SORT1) is a lipoprotein receptor that shows genome-wide association with hypercholesterolemia, explained by its ability to control hepatic output of lipoproteins. Remarkably, SORT1 also shows genome-wide association with Alzheimer disease (AD) and frontotemporal lobe dementia, the most prevalent forms of age-related dementias. Yet, sortilins contribution to human brain lipid metabolism and health remains unclear. Using humanized mouse strains and iPSC-based cell models of brain lipid homeostasis, we document that sortilin mediates neuronal uptake of polyunsaturated fatty acids carried by apoE. Internalized lipids are converted into ligands for PPAR, inducing transcription profiles that enable neurons to use long-chain fatty acids as metabolic fuel. This pathway works with apoE3, but is lost with the AD risk factor apoE4, which disrupts sortilins endocytic activity. We document a role for the lipoprotein receptor sortilin in metabolic fuel choice in neurons, possibly crucial when supply with glucose is limited, as in the aging brain.

neuroscience↗